Clinical features include exertional dyspnea, cough, chest pain, recurrent pneumothorax, chylous pleural effusion, hemoptysis, eventual respiratory failure and, ultimately, death.
英
美
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临床表现有呼吸困难、胸痛、咳嗽、咳血、反覆性气胸、乳糜胸,甚至呼吸衰竭,进而死亡。
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